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Cariotipo 46, XY. Fenotipo femenino. Patologa recesiva ligada al X. La testosterona se metaboliza a estradiol fenotipo femenino Ausencia de receptores de andrognicos. 0+> 0  Introduccin (II)tPresentacin con amenorrea primaria, en etapa neonatal puede presentarse una tumoracin inguinal. Agenesia de tero, trompas de Falopio y tercio superior de vagina Criptorquidia Incremento del riesgo de cncer testicular Tratamiento orquiectoma y terapia de reemplazo hormonal Imgenes: US e IRM. TC poco usada&;Z CObjetivo \Revisar el rol de los mtodos de imagen en el sndrome de feminizacin testicular completo "[] Ecografa Muestra agenesia uterina Permite localizar los testculos no descendidos Puede demostrar lesiones nodulares en las gnadas til en el seguimiento y control de pacientes no orquiectomizadas,b A  Ecografa  Resonancia MagnticaDe eleccin por su capacidad multiplanar y capacidad de contraste de partes blandas Demuestra agenesia de genitales internos (sensibilidad 100%) Caracterizacin de los testculos no descendidos Deteccin de tumores testiculares (sensibilidad >90%) Z Resonancia Magntica Resonancia Magntica  Discusin El sndrome de feminizacin testicular completo debe ser considerado en un contexto de amenorrea primaria Las imgenes pueden demostrar la agenesia de genitales internos y la presencia y ubicacin de testculos no descendidos Es importante buscar y detectar posibles tumores testiculares Z    Conclusin Es importante para el radilogo reconocer los hallazgos del sndrome de feminizacin testicular completo en un contexto de amenorrea primaria, como as tambin buscar y detectar posibles tumores testiculares "  Bibliografa  1. Sadler T. W. Embriologa Mdica. Pg 287-288. 7ma Edicin. Mxico, Editorial Mdica Panamericana. 1996 2. Choi H. K et al MR Imaging of Intersexuality. Radiographics 1998; 18:83-96 3. Tanaka Y et al. Testicular Feminization: Role of MRI in Diagnosing This Rare Male Pseudohermaphroditism. Journal of Computer Assisted Tomography. 22(6):884-888, November/December 1998 4. Koren A el al. Testicular Feminization: Radiologic Considerations in a Unique Form of Cryptorchidism. Abdominal Imaging Vol 21, N3, May 1996, pages 272-274. 5. Karabulut N el al. Stromal Tumor of the Sex Cord in a Woman with Testicular Feminization Syndrome: Imaging Feature. AJR 2002;178:1496-1498 6PP F            $   0` 33` Sf3f` 33g` f` www3PP` ZXdbmo` \ғ3y`Ӣ` 3f3ff` 3f3FKf` hk]wwwfܹ` ff>>\`Y{ff` R>&- {p_/̴>?" dd@,|?" dd@   " @ ` n?" dd@   @@``PR    @ ` ` p>> H@(    6  `}  _+Haga clic para cambiar el estilo de ttulo , ,/  0  `  kHaga clic para modificar el estilo de texto del patrn Segundo nivel Tercer nivel Cuarto nivel Quinto nivel7    l  0ĉ ^ `  X*  0p ^   Z*  0ܓ ^ `  Z*H  0f޽h ? 3380___PPT10.b *Diseo predeterminado} 0  $(  r  S  V>  r  S ^ `    H  0޽h ? 33___PPT10i.b+D=' = @B +}  0 0 $(   r  S & `}   r  S * `  H  0޽h ? 33___PPT10i.2+D=' = @B +  0 @P0(  Px P c $( `}   x P c $ `  H P 0޽h ? 33___PPT10i.2+D=' = @B +}  0 @$(  r  S  `}   r  S T `  H  0޽h ? 33___PPT10i.pT+D=' = @B +}  0 P$(  r  S  `}   r  S , `  H  0޽h ? 33___PPT10i.+D=' = @B +  0 6.P T(  Tx T c $x `}   ^  T 0<  A: Criptorquidia. Imagen nodular hipoecognica en conducto inguinal. B: Tumor testicular. rea heterognea en polo inferior de la gnada (flechas)(2 , eb T C :A"MORRIS_2 cavallo ` T S 8A MORRIS_8 mod@  XB T 0D>p9XB T@ 0D>VXB T 0D>%Sz XB T 0D>Z#  T B,6   5A  T B6  5B H T 0޽h ? 33___PPT10i.+D=' = @B +  0 p\0(  \x \ c $P `}   x \ c $ `  H \ 0޽h ? 33___PPT10i.+D=' = @B +F  0 ]U `(  `x ` c $ `}   x ` s PH$A&cavallo axial t2 2]  z ` s R`A(vassaretto axial t1] ) XB ` 0D)m "XB ` 0D>@5 ` 0 , WCriptorquidia: Imagen nodular (flechas) hipointensa en T1 (A) e hiperintensa en T2 (B) X(2X >     ` 0a &d  7A 2   ` 04c 3  7B 2 H ` 0޽h ? 33___PPT10i.+D=' = @B +$  0 ;3 l(  lx l c $; `}    l 0HC  7A: Agenesia uterina. Imagen sagital en T2 demostrando ausencia de tero. B: Tumor testicular. Imagen axial en T2 que muestra testculo derecho con una imagen isoecognica nodular en su interior (flecha) (2 , f l C >A&cavallo sagital t2w h  l C @A (vassaretto axial t2w  XB  l@ 0D>/3   l 0GS 7  7A 2   l 00LS   7B 2 H l 0޽h ? 33___PPT10i.+D=' = @B +  0 p0(  px p c $Q `}   x p c $Q `  H p 0޽h ? 33___PPT10i.+D=' = @B +$  0 0$(  0r 0 S _ `}   r 0 S  `  H 0 0޽h ? 3380___PPT10.$@:  0 4:(  4r 4 S H `}    4 S B YI  "p`PpH 4 0޽h ? 3380___PPT10.%prH`&A)W.0 $LPN@+a3:= gCIP( f/ 0DArialngs0TT/ܖ 0ܖDWingdings0TT/ܖ 0ܖ6  Arial WingdingsDiseo predeterminado-Sndrome de Feminizacin Testicular CompletoIntroduccin (I)Introduccin (II) Objetivo Ecografa EcografaResonancia MagnticaResonancia MagnticaResonancia Magntica Discusin Conclusin Bibliografa Fuentes usadasPlantilla de diseoTtulos de diapositiva +_㵌0Dr. Ricardo Videla Dr. Ricardo Videla .  2 0SO."SystemH0-@Arial-.  2 0O.-@Arial-. %2 0 ndrome de Feminizaci/ 0DArialngs0TTp5ܖ 0ܖDWingdings0TTp5ܖ 0ܖF  .  @n?" dd@  @@`` p=    $$R$)הR~`O( 9jdR$Q+i UUxcdR$A~#yigzVtƍkR$"j,L V1VR$ `b)'_;#GO$R$؏>U냖T/s+I 0AA@f)))@3ʚ;ʚ;g4PdPd$B 0ppp@ <4dddd w 0TL5 80___PPT10 pp?  %j,Sndrome de Feminizacin Testicular Completo--NElas Salum, Sergio Lucino y Carlos Oulton Instituto Oulton Crdoba, ArgentinaOPOIntroduccin (I)Forma mas frecuente de pseudohermafroditismo masculino (1 cada 20400 nacidos vivos). Cariotipo 46, XY. Fenotipo femenino. Patologa recesiva ligada al X. La testosterona se metaboliza a estradiol fenotipo femenino Ausencia de receptores de andrognicos. 0+ Introduccin (II)~Presentacin con amenorrea primaria, en etapa neonatal puede presentarse una tumoracin inguinal. Agenesia de tero, trompas de Falopio y tercio superior de vagina. Criptorquidia. Incremento del riesgo de cncer testicular. Tratamiento orquiectoma y terapia de reemplazo hormonal. Imgenes: US e IRM. TC poco usada.&@ZObjetivo ]Revisar el rol de los mtodos de imagen en el sndrome de feminizacin testicular completo. "\^ Ecografa Muestra agenesia uterina Permite localizar los testculos no descendidos Puede demostrar lesiones nodulares en las gnadas til en el seguimiento y control de pacientes no orquiectomizadas  Ecografa  Resonancia MagnticaDe eleccin por su capacidad multiplanar y capacidad de contraste de partes blandas Demuestra agenesia de genitales internos (sensibilidad 100%) Caracterizacin de los testculos no descendidos Deteccin de tumores testiculares (sensibilidad >90%) ZResonancia Magntica Resonancia Magntica  Discusin "El sndrome de feminizacin testicular completo debe ser considerado en un contexto de amenorrea primaria. Las imgenes pueden demostrar la agenesia de genitales internos y la presencia y ubicacin de testculos no descendidos. Es importante buscar y detectar posibles tumores testiculares.#Z#   Conclusin Es importante para el radilogo reconocer los hallazgos del sndrome de feminizacin testicular completo en un contexto de amenorrea primaria, como as tambin buscar y detectar posibles tumores testiculares. "  Bibliografa  1. Sadler T. W. Embriologa Mdica. Pg 287-288. 7ma Edicin. Mxico, Editorial Mdica Panamericana. 1996 2. Choi H. K et al MR Imaging of Intersexuality. Radiographics 1998; 18:83-96 3. Tanaka Y et al. Testicular Feminization: Role of MRI in Diagnosing This Rare Male Pseudohermaphroditism. Journal of Computer Assisted Tomography. 22(6):884-888, November/December 1998 4. Koren A el al. Testicular Feminization: Radiologic Considerations in a Unique Form of Cryptorchidism. Abdominal Imaging Vol 21, N3, May 1996, pages 272-274. 5. Karabulut N el al. Stromal Tumor of the Sex Cord in a Woman with Testicular Feminization Syndrome: Imaging Feature. AJR 2002;178:1496-1498 6PP  0 @P0(  Px P c $4r `}   x P c $b `  H P 0޽h ? 33___PPT10i.2+D=' = @B +}  0 @$(  r  S 4 `}   r  S   `  H  0޽h ? 33___PPT10i.pT+D=' = @B +  0 p0(  px p c $" `}   x p c $" `  H p 0޽h ? 33___PPT10i.+D=' = @B +}  0 0$(  0r 0 S  `}   r 0 S  `  H 0 0޽h ? 33___PPT10i.$@+D=' = @B +r(i Yo iRoot EntrydO)Д]PicturesZCurrent User8bSummaryInformation(   !"#$%&'()*+-./012345679._㵌Maria Elena CastrillonMaria Elena Castrillon  2 0SO."SystemH0-@Arial-.  2 0O.-@Arial-. %2 0 ndrome de Feminizaci  !"#$%&'()*+,-./0123456789:;<=>?@ABCDEFGHIJKLMNOPQRSTUVWXYZ[\]^_`abcdefghijklmnopqrstuvwxyz{|}~      !"#$%&'()*+,-./0123456789:;<=>?@ABCDEFGHIJKLMNOPQRSTUVWXYZ[\]^`abcdefghijklmnopqrstuvwxyz{|}~Root EntrydO)@xPicturesZCurrent User8YSummaryInformation( PowerPoint Document(_ٌDocumentSummaryInformation8,F  .  @n?" dd@  @@`` p=    $$R$)הR~`O( 9jdR$Q+i UUxcdR$A~#yigzVtƍkR$"j,L V1VR$ `b)'_;#GO$R$؏>U냖T/s+I 0AA@f)))@3ʚ;ʚ;g4PdPdt< 0ppp@ <4dddd w 0T/ 80___PPT10 pp?  %[,Sndrome de Feminizacin Testicular Completo--NElas Salum, Sergio Lucino y Carlos Oulton Instituto Oulton Crdoba, ArgentinaOPOIntroduccin (I)Forma mas frecuente de pseudohermafroditismo masculino (1 cada 20400 nacidos vivos). Cariotipo 46, XY. Fenotipo femenino. Patologa recesiva ligada al X. La testosterona se metaboliza a estradiol fenotipo femenino Ausencia de receptores de andrognicos. 0+ Introduccin (II)tPresentacin con amenorrea primaria, en etapa neonatal puede presentarse una tumoracin inguinal. Agenesia de tero, trompas de Falopio y tercio superior de vagina Criptorquidia Incremento del riesgo de cncer testicular Tratamiento orquiectoma y terapia de reemplazo hormonal Imgenes: US e IRM. TC poco usada&;ZObjetivo \Revisar el rol de los mtodos de imagen en el sndrome de feminizacin testicular completo "[] Ecografa Muestra agenesia uterina Permite localizar los testculos no descendidos Puede demostrar lesiones nodulares en las gnadas til en el seguimiento y control de pacientes no orquiectomizadas  Ecografa  Resonancia MagnticaDe eleccin por su capacidad multiplanar y capacidad de contraste de partes blandas Demuestra agenesia de genitales internos (sensibilidad 100%) Caracterizacin de los testculos no descendidos Deteccin de tumores testiculares (sensibilidad >90%) ZResonancia Magntica Resonancia Magntica  Discusin El sndrome de feminizacin testicular completo debe ser considerado en un contexto de amenorrea primaria Las imgenes pueden demostrar la agenesia de genitales internos y la presencia y ubicacin de testculos no descendidos Es importante buscar y detectar posibles tumores testiculares Z    Conclusin Es importante para el radilogo reconocer los hallazgos del sndrome de feminizacin testicular completo en un contexto de amenorrea primaria, como as tambin buscar y detectar posibles tumores testiculares "  Bibliografa  1. Sadler T. W. Embriologa Mdica. Pg 287-288. 7ma Edicin. Mxico, Editorial Mdica Panamericana. 1996 2. Choi H. K et al MR Imaging of Intersexuality. Radiographics 1998; 18:83-96 3. Tanaka Y et al. Testicular Feminization: Role of MRI in Diagnosing This Rare Male Pseudohermaphroditism. Journal of Computer Assisted Tomography. 22(6):884-888, November/December 1998 4. Koren A el al. Testicular Feminization: Radiologic Considerations in a Unique Form of Cryptorchidism. Abdominal Imaging Vol 21, N3, May 1996, pages 272-274. 5. Karabulut N el al. Stromal Tumor of the Sex Cord in a Woman with Testicular Feminization Syndrome: Imaging Feature. AJR 2002;178:1496-1498 6PPrQPi( f  !"#$%&'()*+-./012345679Oh+'0 `h  $Sndrome de Feminizacin TesticularSalumDr. Ricardo Videla 96Microsoft Office PowerPoint@AB>@’@@lGt g  9  yf--$xx--'@Arial-.  2 0S."SystemXq-@Arial-.  2 0.-@Arial-. %2 0 ndrome de Feminizaci.-@Arial-.  2 0.-@Arial-.  2 0n .-@Arial-. $2 <$Testicular Completo.-@Arial-.  2 JEl.-@Arial-.  2 J$.-@Arial-. 92 J&!as Salum, Sergio Lucino y Carlos .-@Arial-. 2 PHOulton.-@Arial-. 2 W<Instituto Oulton.-@Arial-.  2 _6C.-@Arial-.  2 _:.-@Arial-. 2 _=rdoba, Argentina.-՜.+,0    XPresentacin en pantalla Workgroupٌ