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Su vinculacin como efecto adverso grave tras la administracin de agentes de contraste relacionados al gadolinio (ACRG) en estudios de Resonancia Magntica (RM) realizados a pacientes con estadios avanzados de insuficiencia renal es motivo de numerosos trabajos de investigacin en los ltimos aos.  P ,H x 0޽h ? AS=S=ιfA)h___PPT10i.-X+D=' = @B +" 0 @<(  "   pPB`0e0e?Title 1 `}  ` ^ Objetivos:    ,   F`0e0e?,Content Placeholder 2 ` ` Reconocer a la FSN como posible efecto adverso grave tras la utilizacin de ACRG y establecer pautas de manejo en pacientes con alteracin en su funcin renal.  ,H x 0޽h ? AS=S=ιfA)h___PPT10i.蠐+D=' = @B +" 0 P&(  *   p4R`0e0e?Title 1 `}  ` fRevisin del tema:  ,    |V`0e0e?,Content Placeholder 2"LFPK!Zf[Content_Types].xmlMO &2WR=cJ`F0iK`#̼vLw 9uSq:w`G ^i ½KI)c/ $oVjTMRc|}042ҥCƔM̏P~*ka/8^DkHbL8e i"K\XN\6rco4y@_;oPK!1_a _rels/.relsj0 ѽqCNo^K [ILcX&m߾0XFo;>0xM e`|X}đ I`߽N4aG2$RKIZ)4(M9`ctB{m:f@`3n|O,ܗr޾jxR0T ,0@}WBLǬ5vPK!O drs/shapexml.xmlWn6;^;'Fc mcaYqAKT"U9Yh}~CiE( 9 ̐SQZWΤNMV臄y3 ?K.溚Xy|jB=`Lb}l,rlX{y`"@ҌVҍ&{P̛ZX$$I*ݤ(m9"nd.#oEK^){ ,c'b+̟+ U( u&Qe{ank@LNoJu!^ba9 F5F*(OE Jt7r :'~8 JmA -f0I 5P= U<p'TAA S̺үp: 4mT8*2 Y+pߟ⑅dQ2e[nPF4w)ٕBHE>y`OuZuƢ3*eY|h4xv@ u]k}7ߊD|j1pLZ/x\+xQ_;􁜂M%/PK-!Zf[Content_Types].xmlPK-!1_a /_rels/.relsPK-!O *drs/shapexml.xmlPK-!L7drs/downrev.xmlPK; ` ` Existe numerosa evidencia cientfica actual que apoya la fuerte asociacin entre la exposicin a ACRG (particularmente gadodiamida) utilizados en RM y la FSN en pacientes con estadios III, IV y V de enfermedad renal crnica (fraccin de filtrado glomerular d" 30 mL/min/1.73 m2) y aguda, en particular en concomitancia con cirugas mayores (ej: periodo peritrasplante heptico), e infeccin. 4 Z u ,H x 0޽h ? AS=S=ιfA)h___PPT10i.+D=' = @B +" 0 /'`(  !   vg`0e0e?Title 1 `}  ` WRevisin del tema  ^   l`0e0e?,Content Placeholder 2*;{M ` x$Esta enfermedad, que compromete principalmente la piel (con cambios que pueden simular una esclerodermia) principalmente de las extremidades, tambin puede afectar otros rganos incluyendo pulmones, corazn, hgado, riones entre otros, con dao variable, incluso la muerte. Actualmente no cuenta con tratamiento efectivo comprobado, aunque se ha probado el uso de prednisona, plasmafresis, talidomida, Ig e.v. en altas dosis as como la inmediata dilisis e incluso el trasplante renal, todas estas opciones de beneficio potencial an en estudio.%%$ ,H x 0޽h ? AS=S=ιfA)h80___PPT10. "  0   ph (     p|`0e0e?Title 1 `}  ` >  z  RA??Picture 2]    Z`>.8cRectangle 3#"@ PK!Zf[Content_Types].xmlMO &2WR=cJ`F0iK`#̼vLw 9uSq:w`G ^i ½KI)c/ $oVjTMRc|}042ҥCƔM̏P~*ka/8^DkHbL8e i"K\XN\6rco4y@_;oPK!1_a _rels/.relsj0 ѽqCNo^K [ILcX&m߾0XFo;>0xM e`|X}đ I`߽N4aG2$RKIZ)4(M9`ctB{m:f@`3n|O,ܗr޾jxR0T ,0@}WBLǬ5vPK!E- drs/shapexml.xmlVMo6 x-ȗ+D^$ҭagMQHڵ I+vXz3y|mF9XSч!gH[5& L%5;?t^6J +/W픁?Ӡs+D@VՠSle6nȒ63ǚ"\IxҊAh^֮ſX97~Nٶ蜳]W(60 zu$"~O&ׄwLoD9~UݠmTrb@(jMuh} Ѫ_cKZm֮Q0܇Gz$K+%Kt$9hV \ሣ[)-$WRBZJe|i@ [p[+Ԫ%~+tX5+O@0"ll#8K|1W#ȕu%Q^H҇e{q}Cn "4O Pr2h .=SA #*ar7BWܹgjP|_Z 8& Mw6 XYtPNdHfDfq#ҥ9݇a{[{erf.׋޼GO1$ej¢4"}^Mkjʟ1ehB-.A ®y44v-ΞI#0s`'P|+t~?rG3gmq+Oꐢ0=`Dގ;H:N _`Ʃ{?'Dj{:&ӽ&XَaaשZHTSktHJ7%C7wCaLf6X< īG {+z&Ig4-aϋQaH\6i)>ѴHPK!Kdrs/downrev.xmlDMk0D^J"7(Jn++zh ox`ёeqauͥy2)ftT۞sꎡ>EUm*/*2觶%:!FWJpY,C-**>Fa.g-˻ D!{̲E9:G)n4ZPK-!Zf[Content_Types].xmlPK-!1_a /_rels/.relsPK-!E- *drs/shapexml.xmlPK-!Kdrs/downrev.xmlPK \  Paciente con FSN que presenta edema, induracin y eritema del antebrazo, y aspecto eritematoso de la piel del muslo que respeta el pliegue inguinal. (Radiology: Volume 243: Number 1 April 2007. 150) E ,1 H x 0޽h ? AS=S=ιfA)h___PPT10i.d+D=' = @B +" 0  O(   #   p@q`0e0e?Title 1 `}  ` _ Conclusin:    ,   ܑ`0e0e?,Content Placeholder 2 ` ` Conclusin: Los ACRG pueden ser administrados en forma relativamente segura. Es importante tener consideracin especial en pacientes con insuficiencia renal. Esto se puede conseguir mediante evaluacin de la necesidad de administrar contraste en estos casos, confirmar la misma luego de visualizar todas las secuencias posibles sin contraste, y en caso de no existir un estudio de imagen alternativo razonable, utilizar la menor dosis efectiva del ACRG menos vinculado a la FSN segn estudios realizados (dimeglumina). En pacientes en dilisis, establecer inmediata dilisis posterior al estudio (aunque no hay prueba cierta que esto pueda prevenir el desarrollo de FSN).*   ,H x 0޽h ? AS=S=ιfA)h___PPT10i.dBg+D=' = @B +". 0 5-$ (  $' $  p0e0e?Title 1 0  W c Bibliografa:   ,^  $  BW0e0e?,Content Placeholder 2 `  W x t 1-Elizabeth A. Sadowski,MD; Lindsey K. Bennett,MD; et al. Nephrogenic Systemic Fibrosis: Risk Factors and Incidence Estimation1. Radiology: Volume 243: Number 1 April 2007. 2-Emanuel Kanal,MD, Dale R. Broome,MD. Response to the FDA s May 23, 2007, Nephrogenic Systemic Fibrosis Update1. Radiology: Volume 246: Number 1 January 2008. 3-Tara Anne Collidge, MBChB, PhD, MRCP, Peter Campbell Thomson, MBChB, BSc(MedSci), MRCP, Patrick Barry Mark, MBChB, BSc(MedSci), MRCP. Gadolinium-enhanced MR Imaging and Nephrogenic Systemic Fibrosis: Retrospective Study of a Renal Replacement Therapy Cohort1. Radiology: Volume 245: Number 1 October 2007. 4-Phillip H. Kuo, MD, PhD, Emanuel Kanal,MD, Ali K. Abu-Alfa,MD. Gadolinium-based MR Contrast Agents and Nephrogenic Systemic Fibrosis1. Radiology: Volume 242: Number 3 March 2007. 5-Dale R. Broome, Mark S. Girguis, Pedro W. Baron. Gadodiamide-Associated Nephrogenic Systemic Fibrosis: Why Radiologists Should Be Concerned. AJR: 188, February 2007. 6-Henrik S. Thomsen. Nephrogenic Sysemic Fibrosis: A Serious Late Adverse Reaction To Gadodiamide. Eur Radiol. 2006 December; 16 (12)2619-2621. 7-Cowper SE. Nephrogenic Sysemic Fibrosing Dermopathy [NFD/NSF]. 2001-2007   " q; U $+ @ Z  U -  &)H x 0޽h ? 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K& _rels/.rels ( 0nS=H^DtiUۛc a)hěBUrdk)Dd gIDr*dS("QlT3Q4b̜'օ9I]e3\0ťQ.D=vtr5aƓI+D#V0;f[e!/PK!tableStyles.xml I0@Ὁwh}-CQ$ +w*!@he/?JXd45ݤ{c@qqi` yߥ0xM e`|X}đ I`߽N4aG2$RKIZ)4(M9`ctB{m:f@`3n|O,ܗr޾jxR0T ,0@}WBLǬ5vPK!*n_ drs/shapexml.xmlVn6;Y'^g6,i  #΢XcΩGRnQ@|3Pzw+Kk2y\ er[1ξ2ikT&w~sU|-l6z6|*l t* `v+(JoFF^#ٯc*_:Q|- Gέ KMZ]('rZ'GB6 | GPgcp(| 2C-;dr2Noގm2S_GY1pfkQb牞iݓ!ekCNI2>Ӌ \qCz1M5.HžL2:rA۪0:g.v><~&W &]mVр ԡ-{LM b^rht|y4r&$'A1pkaE\Qb" cPp=\g B®ծvY=;"±Vx&o\I.CGs%K(sA@4j4qyx}iήRL*vs FRSɤ+wU)Ƿgty[C^D ']>#&tɷi-H R_Vqyԍ+N$`aĞo_.14{h6fa&4$ ]etH*zP}.!G!>߉EPLgK% [%ڰ :e1,4z pMt+xt)3e'5C6v_鰁d'Dg-qND|ƂN߂w\x=SX#_9zYٿn=kw7-ސ/Y3UA  }}'PK!õdrs/downrev.xmlDN0HHܨCUIVP P[`n~Jl{iҷьѷ\SG$ŮԺj* :;6psq'Js4Јֱlb]*,JpHpiʹ֥{4\~M=i^NiзEe>sy1/@ ?_TAn@Uϧp0ܒiPK-!Zf[Content_Types].xmlPK-!1_a /_rels/.relsPK-!*n_ *drs/shapexml.xmlPK-!õ9drs/downrev.xmlPK; ` 5 7La Fibrosis Sistmica Nefrognica (FSN) es una entidad rara, reconocida por primera vez en 1997 y descripta en la literatura a partir del 2000 con alrededor de 250 casos reportados. Su vinculacin como efecto adverso grave tras la administracin de agentes de contraste relacionados al gadolinio (ACRG) en estudios de Resonancia Magntica (RM) realizados a pacientes con estadios avanzados de insuficiencia renal es motivo de numerosos trabajos de investigacin en los ltimos aos.  P ,H x 0޽h ? 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(Radiology: Volume 243: Number 1 April 2007. 150) E.S ,  ,9 ,1 H x 0޽h ? AS=S=ιfA)h___PPT10i.d+D=' = @B +" 0 #$ (  $# $  p`g0e0e?Title 1 0   _ Bibliografa:   ,P  $  0e0e?,Content Placeholder 2 `   j t 1-Elizabeth A. Sadowski,MD; Lindsey K. Bennett,MD; et al. Nephrogenic Systemic Fibrosis: Risk Factors and Incidence Estimation1. Radiology: Volume 243: Number 1 April 2007. 2-Emanuel Kanal,MD, Dale R. Broome,MD. Response to the FDA s May 23, 2007, Nephrogenic Systemic Fibrosis Update1. Radiology: Volume 246: Number 1 January 2008. 3-Tara Anne Collidge, MBChB, PhD, MRCP, Peter Campbell Thomson, MBChB, BSc(MedSci), MRCP, Patrick Barry Mark, MBChB, BSc(MedSci), MRCP. Gadolinium-enhanced MR Imaging and Nephrogenic Systemic Fibrosis: Retrospective Study of a Renal Replacement Therapy Cohort1. Radiology: Volume 245: Number 1 October 2007. 4-Phillip H. Kuo, MD, PhD, Emanuel Kanal,MD, Ali K. Abu-Alfa,MD. Gadolinium-based MR Contrast Agents and Nephrogenic Systemic Fibrosis1. Radiology: Volume 242: Number 3 March 2007. 5-Dale R. Broome, Mark S. Girguis, Pedro W. Baron. Gadodiamide-Associated Nephrogenic Systemic Fibrosis: Why Radiologists Should Be Concerned. AJR: 188, February 2007. 6-Henrik S. Thomsen. Nephrogenic Sysemic Fibrosis: A Serious Late Adverse Reaction To Gadodiamide. Eur Radiol. 2006 December; 16 (12)2619-2621. 7-Cowper SE. Nephrogenic Sysemic Fibrosing Dermopathy [NFD/NSF]. 2001-2007    r9 V%  , > [  h . =   H x 0޽h ? AS=S=ιfA)h___PPT10i.e`i +D=' = @B +"r q  ( / 0DArialiw RomanTTH5ܖ 0ܖDTimes New RomanTTH5ܖ 0ܖD  ՜.+,0t    Presentacin en pantalla   ArialTimes New RomanCalibri Office Theme4Fibrosis sistmica nefrognica asociada a gadolinioIntroduccin: Objetivos:Revisin del tema:Revisin del temaDiapositiva 6 Conclusin:Bibliografa: Fuentes usadasPlantilla de diseoTtulos de diapositiva)_Martha CastrillnMartha Castrillntrillon90e0e?,Content Placeholder 2*;{M  t$Esta enfermedad, que compromete principalmente la piel (con cambios que pueden simular una esclerodermia) principalmente de las extremidades, tambin puede afectar otros rganos incluyendo pulmones, corazn, hgado, riones entre otros, con dao variable, incluso la muerte. Actualmente no cuenta con tratamiento efectivo comprobado, aunque se ha probado el uso de prednisona, plasmafresis, talidomida, Ig e.v. en altas dosis as como la inmediata dilisis e incluso el trasplante renal, todas estas opciones de beneficio potencial an en estudio.%%$ ,H x 0޽h ? 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(Radiology: Volume 243: Number 1 April 2007. 150) E ,1 H x 0޽h ? AS=S=ιfA)h___PPT10i.d+D=' = @B +"\  0 c [ $ (  $# $  p`g0e0e?Title 1 0   _ Bibliografa:   ,  $  0e0e?,Content Placeholder 2 `   t 1-Elizabeth A. Sadowski,MD; Lindsey K. Bennett,MD; et al. Nephrogenic Systemic Fibrosis: Risk Factors and Incidence Estimation1. Radiology: Volume 243: Number 1 April 2007. 2-Emanuel Kanal,MD, Dale R. Broome,MD. Response to the FDA s May 23, 2007, Nephrogenic Systemic Fibrosis Update1. Radiology: Volume 246: Number 1 January 2008. 3-Tara Anne Collidge, MBChB, PhD, MRCP, Peter Campbell Thomson, MBChB, BSc(MedSci), MRCP, Patrick Barry Mark, MBChB, BSc(MedSci), MRCP. Gadolinium-enhanced MR Imaging and Nephrogenic Systemic Fibrosis: Retrospective Study of a Renal Replacement Therapy Cohort1. Radiology: Volume 245: Number 1 October 2007. 4-Phillip H. Kuo, MD, PhD, Emanuel Kanal,MD, Ali K. Abu-Alfa,MD. Gadolinium-based MR Contrast Agents and Nephrogenic Systemic Fibrosis1. 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